Professor Julie Snowden
julie.snowden@manchester.ac.uk
Professor Julie Snowden is a Consultant Neuropsychologist and Honorary Professor of Neuropsychology. Professor Snowden was instrumental in establishing the Cerebral Function Unit as a multi-disciplinary diagnostic clinic in the early 1980s. Her special interest is in young-onset degenerative brain disorders and their associated cognitive and behavioural changes. She has played an important role in the characterisation of focal degenerative disorders including frontotemporal dementia and progressive aphasic syndromes. Her experimental studies of semantic dementia have increased understanding of the interrelationship between language and memory. She helped to establish a multidisciplinary research clinic into Huntington’s disease and remains involved in the Neuropsychological Working Group for the European Huntington’s disease network.
She has published more than 140 scientific papers and book chapters and is first author of a clinical monograph on frontotemporal lobe degeneration.
Professor Snowden is a practitioner member of the British Psychological Society Division of Neuropsychology. She is a member of a number of International research organisations including the World Federation of Neurology research group into Aphasia and Cognitive Disorders and the Memory Disorders Research Society.
Selected publications
Books
Snowden JS, Neary D, Mann DMA. Fronto-temporal lobar degeneration: fronto-temporal dementia, progressive aphasia, semantic dementia. London: Churchill-Livingstone 1996.
Academic Journal articles
Snowden JS, Stopford C, Julien C, Thompson JC, Davidson Y, Gibbons L, Prichard A, Lendon CL, Richardson A, Varma A, Neary D, Mann DMA. Cognitive phenotypes in Alzheimer’s disease and Genetic Risk. Cortex, in press.
Stopford CL, Snowden JS, Thompson JC, Neary D. Variability in cognitive presentation of Alzheimer’s disease. Cortex, in press.
Stopford CL, Snowden JS, Thompson JC, Neary D. Distinct memory profiles in Alzheimer’s disease. Cortex, in press.
Gibbons ZC, Snowden JS, Thompson JC, Happé F, Richardson A, Neary D. Inferring thought and action in motor neuron disease. Neuropsychologia, 2007; 45: 1196-1207.
Julien CL, Thompson JC, Wild S, Yardumian P, Snowden JS, Turner G, Craufurd C. Psychiatric disorders in pre-clinical Huntington's Disease. Journal of Neurology, Neurosurgery and Psychiatry, doi:10.1136/jnnp.2006.103309
Snowden JS, Pickering-Brown SM, Mackenzie I, Richardson A, Varma A, Neary D, Mann DMA. Progranulin gene mutations associated with frontotemporal dementia and progressive non fluent aphasia. Brain 2006 in press
Baker M, Mackenzie IR, Pickering-Brown SM, Gass J, Rademakers R, Lindholm C, Snowden J, Adamson J, Sadovnick AD, Rollinson S, Cannon A, Dwosh E, Neary D, Melquist S, Richardson A, Dickson D, Berger Z, Eriksen J, Robinson T, Zehr C, Dickley CA, Crook R, McGowan E, Mann D, Boeve Bradley, Feldham H, Hutton M. Mutations in progranulin cause tau-negative frontotemporal dementia linked to chromosome 17. Nature, 2006; 442: 916-919.
Snowden JS, Neary D, Mann DMA. Autopsy proven, sporadic frontotemporal dementia, due to microvacuolar histology, with onset at 21 years of age. Journal of Neurology, Neurosurgery and Psychiatry 2004; 75:1337-9.
Snowden JS, Thompson JC, Neary D. Knowledge of famous faces and names in semantic dementia. Brain 2004; 127:860-872.
Snowden JS, Gibbons ZC, Blackshaw A, Doubleday E, Thompson J, Craufurd D, Foster J, Happé F, Neary D. Social cognition in frontotemporal dementia and Huntington’s disease. Neuropsychologia 2003; 41:688-701.
Snowden JS, Neary D. Progressive anomia with preserved oral spelling and automatic speech. Neurocase 2003:9:27-43.
Doubleday EK, Snowden JS, Varma AR, Neary D. Qualitative performance characteristics differentiate dementia with Lewy bodies and Alzheimer’s disease. Journal of Neurology, Neurosurgery and Psychiatry 2002; 72:602-607.
Snowden JS, Craufurd D, Thompson J, Neary D. Psychomotor, executive and memory function in preclinical Huntington's disease. Journal of Clinical and Experimental Neuropsychology 2002; 24:133-145.
Snowden JS, Neary D. Relearning of verbal labels in semantic dementia. Neuropsychologia 2002; 40:1715-1728.
Snowden JS, Mann DMA, Neary D. Distinct neuropsychological characteristics in Creutzfeldt-Jakob disease. Journal of Neurology, Neurosurgery and Psychiatry 2002; 73:686-694.
Bathgate D, Snowden JS, Varma A, Blackshaw A, Neary D. Behaviour in frontotemporal dementia: a comparison with Alzheimer's disease and vascular dementia. Acta Neurologica Scandinavica 2001; 103:367-378
Snowden JS, Bathgate B, Varma A, Blackshaw A, Gibbons ZC, Neary D. Distinct behavioural profiles in frontotemporal dementia and semantic dementia. Journal of Neurology, Neurosurgery and Psychiatry 2001; 70:323-332.
Snowden JS, Craufurd D, Griffiths HL, Thompson J, Neary D. Longitudinal evaluation of cognitive disorder in Huntington's disease. Journal of the International Neuropsychological Society 2000; 6: 33-44.
Snowden JS, Griffiths HL, Neary D. The role of autobiographical experience on meaning. Cognitive Neuropsychology 1999; 16: 673-687.
Hutton M, Lendon CL, Rizzu P et al. Association of missense and 5'-splice mutations in tau with the inherited FTDP-17. Nature 1998; 393: 702-705.
Neary D, Snowden JS, Gustafson L, Passant U, Stuss D, Black S, Freedman M, Kertesz A, Robert PH, Albert M, Boone K, Miller BL, Cummings J, Benson DF. Frontotemporal lobar degeneration. A consensus on clinical diagnostic criteria. Neurology 1998; 51: 1546-1554.
Snowden JS, Craufurd D, Griffiths HL, Neary D. Awareness of involuntary movements in Huntington’s disease. Archives of Neurology 1998; 55: 801-805.
Snowden JS, Griffiths HL, Neary D. Semantic-episodic memory interactions in semantic dementia: implications for retrograde memory function. Cognitive Neuropsychology 1996; 8: 1101-1137.
Snowden JS, Griffiths HL, Neary D. Progressive language disorder associated with frontal lobe degeneration. Neurocase 1996; 2: 429-440.
Review Articles
Neary D, Snowden JS, Mann DMA. Frontotemporal dementia. Lancet Neurology 2005; 4:771-80.
Snowden JS, Neary D, Mann DMA. Frontotemporal dementia. British Journal of Psychiatry 2002; 180:140-143
Snowden JS. Commentary on Liepmann 1908 and Rosenfeld 1909. Cortex 2001; 37:563-71.
Snowden JS. Neuropsychological evaluation and the diagnosis and differential diagnosis of dementia. Reviews in Clinical Gerontology 1999; 9:65-72.
Snowden JS, Neary D. Neuropsychiatric aspects of frontotemporal dementias. Current Psychiatry Reports 1999; 1:93-98.
Book chapters
Snowden JS, Kindell J, Neary D. Diagnosing semantic dementia and managing communication difficulties. In K Bryan, J Maxim (eds) Communication Disability in the Dementias Chichester: Wiley 2006 125-146.
Snowden JS. Semantic dementia. In O’Brien J, Ames D, Burns A (eds) Dementia Kluwer Academic and Lippincott-Raven Publishers; 3nd edition 2005 Chapter 55 pp 702-712; 2nd edition 2000 Chapter 59, pp 769-778.
Craufurd D, Snowden JS. Neuropsychological and neuropsychiatric aspects of Huntington's disease. In P Harper, G Bates & L Jones (eds.) Huntington's disease 3rd edition, Oxford: Oxford University Press 2002, 62-94
Snowden JS. Disorders of semantic memory. In A Baddeley, B Wilson, M. Kopelman (eds) Handbook of Memory Disorders 2nd edition, Chichester: John Wiley. 2002 pp 293-314.
Snowden JS, Griffiths HL. Semantic dementia: assessment and management. In Best W, Bryan K, Maxim J (eds) Semantic processing: theory and practice, 2001
Neary D, Snowden JS. Progressive Focal Cortical Syndromes. In WG Bradley, RB Daroff, GM Fenichel, CD Marsden (eds) Neurology in Clinical Practice: Principles of Diagnosis and Management Third edition. Butterworth-Heinemann 1999.
